Myelopathy in mucopolysaccharidosis type II (Hunter syndrome)

Clarence E. Ballenger; Thomas R. Swift; Robert T. Leshner; Taher A. El Gammal; Thomas F. McDonald

doi:10.1002/ana.410070418

Myelopathy in mucopolysaccharidosis type II (Hunter syndrome)

Clarence E. Ballenger, Thomas R. Swift, Robert T. Leshner, Taher A. El Gammal, Thomas F. McDonald

Neurology

Research output: Contribution to journal › Article › peer-review

24 Scopus citations

Abstract

A 24‐Year‐old man with Hunter syndrome had spastic quadriparesis due to impingement of thickened meninges upon the cervical spinal cord. Tracheal narrowing due to submucosal deposits (presumably mucopolysaccharide) produced serious ventilatory complications during induction of anesthesia and necessitated tracheostomy before surgical decompression of the spinal cord could be attempted. Recognition of compressive myelopathy and tracheal compromise as late complications of Hunter syndrome may promote early therapy and prevent respiratory catastrophe.

Original language	English (US)
Pages (from-to)	382-385
Number of pages	4
Journal	Annals of Neurology
Volume	7
Issue number	4
DOIs	https://doi.org/10.1002/ana.410070418
State	Published - Apr 1980

ASJC Scopus subject areas

Neurology
Clinical Neurology

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10.1002/ana.410070418

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AU - Swift, Thomas R.

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AU - El Gammal, Taher A.

AU - McDonald, Thomas F.

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AB - A 24‐Year‐old man with Hunter syndrome had spastic quadriparesis due to impingement of thickened meninges upon the cervical spinal cord. Tracheal narrowing due to submucosal deposits (presumably mucopolysaccharide) produced serious ventilatory complications during induction of anesthesia and necessitated tracheostomy before surgical decompression of the spinal cord could be attempted. Recognition of compressive myelopathy and tracheal compromise as late complications of Hunter syndrome may promote early therapy and prevent respiratory catastrophe.

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ER -

Myelopathy in mucopolysaccharidosis type II (Hunter syndrome)

Abstract

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