Goodpasture syndrome involving overlap with Wegener's granulomatosis and anti-glomerular basement membrane disease
- Raghu Kalluri(corresponding author),
- Kevin Meyers,
- Andras Mogyorosi,
- Michael P. Madaio,
- Eric G. Neilson
- Harvard University,
- University of Pennsylvania
Open access
Abstract
A 68-year-old Caucasian woman presented to the hospital with nodular pulmonary infiltrates and acute renal failure. Wegener's granulomatosis was initially considered to be most likely because of the presence of increased serum levels of c-anti-neutrophil cytoplasmic antibodies (c-ANCA). A consultation through the Internet after a renal biopsy demonstrated crescentic, necrotizing glomerulonephritis and linear deposits of immunoglobulin G (IgG) and complement C3, typical of anti-glomerular basement membrane (GBM) disease. Hemodialysis was instituted; however, the patient suddenly developed a massive cerebral hemorrhage and died before full therapy could take effect. Postmortem analysis of the patient's sera revealed high titers of IgG against the α3 NC1 domain of type IV collagen. Serologic evidence of both p-ANCA and anti-GBM antibodies are becoming more frequently recognized in the setting of rapidly progressive glomerulonephritis. The patient reported here had the unusual combination of c-ANCA antibodies with anti-GBM disease, and this association raises complex questions regarding the pathogenesis of this type of renal injury.
Publication Information
Output type
Original language
English (US)Pages from-to (Number of pages)
Pages 1795-1800 (6 pages)Journal (Volume, Issue Number)
Journal of the American Society of Nephrology (Volume 8, Issue 11)Publication milestones
- Published - 11/1997
Publication status
ISSN
1046-6673Publication IDs
- Scopus: 0030716935
- PubMed: 9355084
