TY - JOUR
T1 - A case report of Y-shaped bi-directional Fontan procedure
T2 - promising long-term outcomes for single ventricle physiology patients
AU - Agarwal, Abhimanyu
AU - Cribbs, Marc
AU - Ahmed, Asmaa Naguib
AU - Abozeed, Mostafa
N1 - Publisher Copyright:
© 2023, The Author(s).
PY - 2023/12
Y1 - 2023/12
N2 - Background: Achieving optimal hepatic factor distribution and total cavopulmonary resistance is crucial for long-term outcomes in single ventricle palliation patients. Y-shaped Gore-Tex Fontan procedure redirects hepatic drainage to both the right and left pulmonary arteries. The aim of this approach is to achieve bilateral pulmonary distribution of hepatic factors and reduce the risk of arteriovenous malformations that can develop in single-ventricle patients. Case presentation: We present a unique case of a 20 years old female with symptoms of heart failure, who has a history of complex heterotaxy with polysplenia, interrupted Inferior vena-cava, and double outlet right ventricle with unbalanced atrio-ventricular septal defect, d-malposed great arteries, and pulmonary atresia. Fenestrated Y-shaped Gore-Tex Fontan procedure was successfully done which was confirmed by performing cardiac CT angiography. Conclusions: Studies have shown that achieving balanced hepatic factor distribution and low resistance in the Fontan pathway can improve long-term outcomes. This procedure has demonstrated positive results in terms of oxygen saturation and reduced asymmetric blood flow distribution. Level of Evidence: Level 4, Case Report.
AB - Background: Achieving optimal hepatic factor distribution and total cavopulmonary resistance is crucial for long-term outcomes in single ventricle palliation patients. Y-shaped Gore-Tex Fontan procedure redirects hepatic drainage to both the right and left pulmonary arteries. The aim of this approach is to achieve bilateral pulmonary distribution of hepatic factors and reduce the risk of arteriovenous malformations that can develop in single-ventricle patients. Case presentation: We present a unique case of a 20 years old female with symptoms of heart failure, who has a history of complex heterotaxy with polysplenia, interrupted Inferior vena-cava, and double outlet right ventricle with unbalanced atrio-ventricular septal defect, d-malposed great arteries, and pulmonary atresia. Fenestrated Y-shaped Gore-Tex Fontan procedure was successfully done which was confirmed by performing cardiac CT angiography. Conclusions: Studies have shown that achieving balanced hepatic factor distribution and low resistance in the Fontan pathway can improve long-term outcomes. This procedure has demonstrated positive results in terms of oxygen saturation and reduced asymmetric blood flow distribution. Level of Evidence: Level 4, Case Report.
KW - Arteriovenous malformation
KW - Case report
KW - Cavopulmonary resistance
KW - Multiplanar reconstructions
KW - Y-shaped bidirectional Fontan graft
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U2 - 10.1186/s43055-023-01059-0
DO - 10.1186/s43055-023-01059-0
M3 - Article
AN - SCOPUS:85163963694
SN - 0378-603X
VL - 54
JO - Egyptian Journal of Radiology and Nuclear Medicine
JF - Egyptian Journal of Radiology and Nuclear Medicine
IS - 1
M1 - 115
ER -