Clinical Spectrum of VCP Myopathy, Paget Disease, and Frontotemporal Dementia: Experimental Models and Potential Treatments

Virginia E. Kimonis, Eric Dec, Mallikarjun Badadani, Angele Nalbandian, Jouni Vesa, Vincent Caiozzo, Douglas Wallace, Barbara Martin, Charles Smith, Giles D. Watts

Research output: Chapter in Book/Report/Conference proceedingChapter

Original languageEnglish (US)
Title of host publicationMuscle Aging, Inclusion-Body Myositis and Myopathies
PublisherWiley-Blackwell
Pages219-229
Number of pages11
ISBN (Print)1405196467, 9781405196468
DOIs
StatePublished - Dec 19 2011
Externally publishedYes

Keywords

  • Autophagy
  • ERAD
  • Endoplasmic reticulum-associated degradation
  • Frontotemporal dementia
  • Inclusion-body myopathy
  • Paget disease of bone
  • TAR DNA-binding protein 43
  • TDP-43
  • Ubiquitin-proteasome system
  • Valosin-containing protein

ASJC Scopus subject areas

  • General Neuroscience

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