Papillary fibroelastoma of tricuspid valve in a pediatric patient

We are reporting a rare case of papillary fibroelastoma of the tricuspid valve in an 8-year-old child who presented with pulmonary embolism. Echocardiography was instrumental in determining the source of the pulmonary embolism, but not in delineating between tumor and thrombus. Successful surgical resection of the mass was accomplished and good outcome was attained despite the delay in diagnosis and failure of medical management. A high index of suspicion for tumor involving the tricuspid valve is emphasized despite its rarity in children.